Variant creutz feldt jacob disease


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VARIANT CREUTZ FELDT JACOB DISEASE

  • young patients <30 years*
    Rapid mental deterioration and dementia
    myoclonus
    psychological symptoms- anxiety, withdrawal
    akinetic mutism

MRI- HOCKEY STICK SIGN- posterior thalamic changes (bilateral pulvinar high intensity signals) picture
Tonsil biopsy- Prion proteins (picture)
Px. Poor. Death in 13 months
Treatment- none :frowning:
Symptomatic. Palliative.

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