Common deformity in chiari H
malformation is -
a) Syringomyelia
b) Meningo myelocele
c) Hydrocephalus
d) All of above
Correct Answer - D
Answer- D. All of above
Chiari malformation is divided into :
- Type I : Produce symptoms during adolescence or adulthood is
usually not associated with hydrocephalus. The deformity consists of
displacement of cerebellar tonsils into the cervical canal. - Type II : It is characterized by progressive hydrocephalus with a
myelomeningocele in newborns. There is a failure of pontine flexure
during embryogenensis, which results in elongation of 4th ventricle;
kinking of brainstem and breaking of quadrigeminal plate (tectum);
along with displacement of inferior vermis, pons and medulla into
cervical canal. This causes widening of cervical canal
(syringomyelia). - Type III : Usually associated with occipital encephalocele and
causes abundant neurological deficit. - Type IV : Characterised by lack of cerebeller development and
usually not compatable with life.