Identify the heart disorder with following specification

Identify the heart disorder with following specifications

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1.Tricupid atresia
2.Ebetein anomaly
3.TOF
4.ASD

Solution:

Apical displacement of the septal leaflet of tricuspid leaflet of greater than 8 mm/m2- Most specific sign

Ebstein anomaly is a congenital malformation of the heart that is characterized by apical displacement of the septal and posterior tricuspid valve leaflets, leading to atrialization of the right ventricle with a variable degree of malformation and displacement of the anterior leaflet .

There is often severe right sided cardiomegaly due to an elongated and enlarged right atrium tiich may result in an elevated apex Classically, the heart is described as having a “box shape” on a frontal chest radiograph.